Double outlet right ventricle
3417994
190228277
2008-02-09T19:24:44Z
JNW
1905157
Reverted edits by [[Special:Contributions/Bnationalp|Bnationalp]] ([[User talk:Bnationalp|talk]]) to last version by LordAnubisBOT
{{Infobox_Disease |
Name = {{PAGENAME}} |
Image = |
Caption = |
DiseasesDB = 32215 |
ICD10 = {{ICD10|Q|20|1|q|20}} |
ICD9 = {{ICD9|745.11}} |
ICDO = |
OMIM = 217095 |
MedlinePlus = |
eMedicineSubj = ped |
eMedicineTopic = 2509 |
eMedicine_mult = {{eMedicine2|ped|2508}} |
MeshID = D004310 |
}}
'''Double outlet right ventricle''' ('''DORV''') is a form of [[congenital heart disease]] where both of the [[great arteries]] connect (in whole or in part) to the [[right ventricle]] (RV).
== Anatomy and pathophysiology ==
DORV occurs in a multiple forms, with variability of great artery position and size, as well as of [[ventricular septal defect]] (VSD) location. It can occur with or without [[transposition of the great arteries]]. The clinical manifestations are similarly variable, depending on how the anatomical defects affect the [[physiology]] of the heart, in terms of altering the normal flow of blood from the RV and [[left ventricle]] (LV) to the [[aorta]] and [[pulmonary artery]]. For example:
:*in DORV with a [[wiktionary:subaortic|subaortic]] VSD, blood from the LV flows through the VSD to the aorta and blood from the RV flows mainly to the pulmonary artery, yielding physiology similar to [[Tetralogy of Fallot]]
:*in DORV with a [[wiktionary:subpulmonic|subpulmonic]] VSD (called '''[[Taussig-Bing syndrome]]'''), blood from the LV flows through the VSD to the pulmonary artery and blood from the RV flows mainly to the aorta, yielding physiology similar to [[Transposition of the Great Arteries]]
:**but if there is [[pulmonic stenosis]] in addition, physiology resembles [[Tetralogy of Fallot]]
:*in other forms of DORV, blood from both ventricles is substantially mixed in the RV, yielding physiology that resembles a large VSD
:**but again, if there is [[pulmonic stenosis]], physiology resembles [[Tetralogy of Fallot]]
==External links==
* {{WhoNamedIt|synd|2285}}
* [http://www.rch.org.au/cardiology/defects.cfm?doc_id=5087 Illustrations at rch.org.au]
[[Category:Congenital heart disease]]
{{circulatory-stub}}
{{Congenital malformations and deformations of circulatory system}}
[[de:Double outlet right Ventricle]]
[[fr:Ventricule droit à double sortie]]
[[uk:Подвійне відходження магістральних судин від правого шлуночку]]