Double outlet right ventricle 3417994 190228277 2008-02-09T19:24:44Z JNW 1905157 Reverted edits by [[Special:Contributions/Bnationalp|Bnationalp]] ([[User talk:Bnationalp|talk]]) to last version by LordAnubisBOT {{Infobox_Disease | Name = {{PAGENAME}} | Image = | Caption = | DiseasesDB = 32215 | ICD10 = {{ICD10|Q|20|1|q|20}} | ICD9 = {{ICD9|745.11}} | ICDO = | OMIM = 217095 | MedlinePlus = | eMedicineSubj = ped | eMedicineTopic = 2509 | eMedicine_mult = {{eMedicine2|ped|2508}} | MeshID = D004310 | }} '''Double outlet right ventricle''' ('''DORV''') is a form of [[congenital heart disease]] where both of the [[great arteries]] connect (in whole or in part) to the [[right ventricle]] (RV). == Anatomy and pathophysiology == DORV occurs in a multiple forms, with variability of great artery position and size, as well as of [[ventricular septal defect]] (VSD) location. It can occur with or without [[transposition of the great arteries]]. The clinical manifestations are similarly variable, depending on how the anatomical defects affect the [[physiology]] of the heart, in terms of altering the normal flow of blood from the RV and [[left ventricle]] (LV) to the [[aorta]] and [[pulmonary artery]]. For example: :*in DORV with a [[wiktionary:subaortic|subaortic]] VSD, blood from the LV flows through the VSD to the aorta and blood from the RV flows mainly to the pulmonary artery, yielding physiology similar to [[Tetralogy of Fallot]] :*in DORV with a [[wiktionary:subpulmonic|subpulmonic]] VSD (called '''[[Taussig-Bing syndrome]]'''), blood from the LV flows through the VSD to the pulmonary artery and blood from the RV flows mainly to the aorta, yielding physiology similar to [[Transposition of the Great Arteries]] :**but if there is [[pulmonic stenosis]] in addition, physiology resembles [[Tetralogy of Fallot]] :*in other forms of DORV, blood from both ventricles is substantially mixed in the RV, yielding physiology that resembles a large VSD :**but again, if there is [[pulmonic stenosis]], physiology resembles [[Tetralogy of Fallot]] ==External links== * {{WhoNamedIt|synd|2285}} * [http://www.rch.org.au/cardiology/defects.cfm?doc_id=5087 Illustrations at rch.org.au] [[Category:Congenital heart disease]] {{circulatory-stub}} {{Congenital malformations and deformations of circulatory system}} [[de:Double outlet right Ventricle]] [[fr:Ventricule droit à double sortie]] [[uk:Подвійне відходження магістральних судин від правого шлуночку]]