Hepatosplenomegaly 1018486 225975144 2008-07-16T08:01:15Z Thijs!bot 1392310 robot Adding: [[cs:Hepatosplenomegalie]] {{DiseaseDisorder infobox | Name = Hepatosplenomegaly | ICD10 = {{ICD10|R|16|2|r|10}} | ICD9 = {{ICD9|571.8}}, {{ICD9|789.1}}, {{ICD9|789.2}} | ICDO = | Image = | Caption = | OMIM = | MedlinePlus = 003275 | eMedicineSubj = | eMedicineTopic = | DiseasesDB = | }} '''Hepatosplenomegaly''' is the simultaneous enlargement of both the [[liver]] ([[hepatomegaly]]) and the [[spleen]] ([[splenomegaly]]). ==Differential diagnosis== {{Expand list}} # A # Aagenaes syndrome ... enlarged liver # Acanthocytosis ... enlarged spleen, enlarged liver # Acidemia, methylmalonic ... enlarged liver # Acquired idiopathic sideroblastic anaemia ... enlarged spleen, enlarged liver # Acquired total lipodystrophy ... enlarged liver # Acral dysostosis - dyserythropoiesis ... enlarged spleen, enlarged liver # Acromegaly ... enlarged spleen, enlarged liver # Actinomycetales infection ... enlarged spleen, enlarged liver # Acute biphenotypic leukemia ... enlarged spleen, enlarged liver # Acute cholinergic dysautonomia ... enlarged spleen, enlarged liver # Acute leukaemia of ambiguous lineage ... enlarged spleen, enlarged liver # Acute lymphoblastic leukemia ... enlarged spleen, enlarged liver # Acute lymphoblastic leukemia, adult ... enlarged spleen, enlarged liver # Acute megacaryoblastic leukemia ... enlarged spleen, enlarged liver # Acute myeloblastic leukemia type 1 ... enlarged spleen, enlarged liver, enlarged liver # Acute myeloblastic leukemia type 2 ... enlarged spleen, enlarged liver # Acute myeloblastic leukemia type 3 ... enlarged spleen, enlarged liver # Acute myeloblastic leukemia type 4 ... enlarged spleen, enlarged liver # Acute myeloblastic leukemia type 5 ... enlarged spleen, enlarged liver # Acute myeloblastic leukemia type 6 ... enlarged spleen, enlarged liver # Acute myeloblastic leukemia type 7 ... enlarged spleen, enlarged liver # Acute myelocytic leukemia ... enlarged spleen, enlarged liver, enlarged liver, enlarged liver # Acute myelofibrosis ... enlarged spleen, enlarged liver # Acute myeloid leukaemia and myelodysplastic syndromes related to alkylating agent ... enlarged spleen, enlarged liver # Acute myeloid leukaemia and myelodysplastic syndromes related to topoisomerase type II inhibitor ... enlarged spleen, enlarged liver # Acute myeloid leukaemia and myelodysplastic syndromes, therapy related ... enlarged spleen, enlarged liver # Acute myeloid leukemia ... enlarged spleen, enlarged liver # Acute myeloid leukemia, adult ... enlarged spleen, enlarged liver # Acute myelosclerosis ... enlarged spleen # Acute panmyelosis ... enlarged spleen, enlarged liver # Acute vitamin A toxicity ... enlarged liver # Addison-Gull syndrome ... enlarged spleen, enlarged liver # Adrenoleukodystrophy ... enlarged liver # Adrenoleukodystrophy, autosomal, neonatal form ... enlarged liver # Adult onset Still's disease ... enlarged spleen, enlarged liver # African Sleeping sickness ... enlarged spleen # Aggressive NK-cell leukaemia ... enlarged spleen, enlarged liver # Aggressive systemic mastocytosis ... enlarged spleen, enlarged liver # Aicardi-Goutieres syndrome 1 ... enlarged spleen, enlarged liver # Aicardi-Goutieres syndrome 2 ... enlarged spleen, enlarged liver # Aicardi-Goutieres syndrome 3 ... enlarged spleen, enlarged liver # Aicardi-Goutieres syndrome 4 ... enlarged spleen, enlarged liver # Aicardi-Goutieres syndrome 5 ... enlarged spleen, enlarged liver # Alagille Syndrome ... enlarged spleen, enlarged liver # Albers-Schonberg disease - malignant recessive form ... enlarged spleen, enlarged liver, enlarged liver # Alcohol-induced pseudo-Cushing syndrome ... enlarged liver # Aldolase A deficiency ... enlarged spleen, enlarged liver # ALL-Down syndrome ... enlarged spleen, enlarged liver # Alpha-mannosidosis type II ... enlarged liver # Amyloidosis ... enlarged spleen, enlarged liver # Amyloidosis, familial visceral ... enlarged spleen, enlarged liver # Andersen disease ... enlarged spleen, enlarged liver, enlarged liver # Anemia, hypochromic microcytic ... enlarged spleen # Anemia, Neonatal ... enlarged spleen, enlarged liver # Anemia, Sideroblastic ... enlarged spleen, enlarged liver # Angioimmunoblastic with dysproteinemia lymphadenopathy ... enlarged liver and spleen # Angiosarcoma of the liver ... enlarged liver # Apo A-I deficiency ... enlarged spleen # Arakawa's syndrome 2 ... enlarged spleen, enlarged liver # AREDYLD ... enlarged liver # Arginase deficiency ... enlarged liver # Argininosuccinase lyase deficiency, neonatal ... enlarged liver # Argininosuccinic aciduria ... enlarged liver # Arthralgia - purpura - weakness syndrome ... enlarged spleen # Aspartylglycosaminuria ... enlarged spleen, enlarged liver # Asrar-Facharzt-Haque syndrome ... enlarged spleen, enlarged liver # Athabaskan severe combined immunodeficiency ... enlarged liver # Autoimmune Hepatitis ... enlarged liver # Autoimmune Lymphoproliferative Syndrome ... enlarged spleen, enlarged liver # Autoimmune Thrombocytopenia ... enlarged spleen TopB # Baker-Winegrad disease ... enlarged liver # Ballard syndrome ... enlarged spleen, enlarged liver # Banti's syndrome ... enlarged spleen, enlarged liver, enlarged liver # Bantu siderosis ... enlarged liver # Bartonella ... enlarged liver # Bartonellosis ... enlarged spleen, enlarged liver # Bearn-Kunkel syndrome ... enlarged spleen, enlarged liver # Benign intrahepatic cholestasis type 1 ... enlarged liver # Benign intrahepatic cholestasis type 2 ... enlarged liver # Berardinelli-Seip congenital lipodystrophy ... enlarged liver # Berardinelli-Seip congenital lipodystrophy, type 1 ... enlarged liver # Berardinelli-Seip congenital lipodystrophy, type 2 ... enlarged liver # Bernheim's syndrome ... enlarged liver # Besnier-Boeck-Schaumann disease ... enlarged spleen, enlarged liver # Bile acid synthesis defects ... enlarged spleen, enlarged liver # Bile acid synthesis defects, congenital, 1 ... enlarged spleen, enlarged liver # Bile acid synthesis defects, congenital, 2 ... enlarged spleen, enlarged liver # Bile acid synthesis defects, congenital, 3 ... enlarged spleen, enlarged liver # Bile acid synthesis defects, congenital, 4 ... enlarged spleen, enlarged liver # Bile Duct Cancer ... Enlarged liver # Bile Duct Conditions ... Enlarged liver # Bile plug syndrome ... enlarged liver # Biliary Atresia ... enlarged liver # Biliary atresia, intrahepatic, non syndromic form ... enlarged liver # Biliary atresia, intrahepatic, syndromic form ... enlarged liver # Biliary disorder ... Enlarged liver # Biliary hypoplasia ... enlarged liver # Blastoma ... enlarged spleen, enlarged liver # Brucellosis ... enlarged spleen, enlarged liver, enlarged liver # Brunzell syndrome ... enlarged spleen, enlarged liver # Budd-Chiari syndrome ... enlarged spleen, enlarged liver, enlarged liver TopC # Camurati-Engelmann Disease ... enlarged liver and spleen # Carbamoyl-phosphate synthase 1 deficiency ... enlarged liver # Carcinoid syndrome ... enlarged liver # Cardiomyopathy - hypogonadism - metabolic anomalies ... enlarged liver # Cardiomyopathy - spherocytosis ... enlarged spleen, enlarged liver # Cardiomyopathy due to anthracyclines ... enlarged liver # Carnitine palmitoyl transferase 1 deficiency ... enlarged liver # Carnitine palmitoyl transferase 2 deficiency ... enlarged liver # Carnitine palmitoyl transferase deficiency ... enlarged liver # Carnitine palmitoyl transferase II deficiency, infantile hepatocardiomuscular type ... enlarged liver # Carnitine-acylcarnitine translocase deficiency ... enlarged liver # Caroli Disease ... enlarged liver # Caspase-8 deficiency ... enlarged spleen # Castellani syndrome ... enlarged spleen, enlarged liver # CCF ... enlarged liver # CDG syndrome (generic term) ... enlarged spleen, enlarged liver # Cerebrorenodigital syndrome ... enlarged spleen # Chédiak-Higashi syndrome ... enlarged liver # Chagas disease ... enlarged spleen, enlarged liver, Hepatosplenomegaly # Cholestasis, progressive familial intrahepatic 1 ... enlarged spleen, enlarged liver # Cholestasis, progressive familial intrahepatic 2 ... enlarged spleen, enlarged liver # Cholestasis, progressive familial intrahepatic 3 ... enlarged spleen, enlarged liver # Choriocarcinoma, infantile ... enlarged liver # Chronic Fatigue Syndrome ... enlarged liver # Chronic Granulomatous Disease ... enlarged spleen, enlarged liver, enlarged liver # Chronic Hepatitis C ... Enlarged spleen, Enlarged liver # Chronic lymphocytic leukemia ... enlarged spleen # Chronic myelogenous leukemia ... enlarged spleen # Chronic myelomonocytic leukemia ... enlarged spleen, enlarged liver # Chronic Myeloproliferative Disorders ... enlarged spleen # Chronic vitamin A toxicity ... enlarged liver # Cirrhosis of the liver ... Enlarged spleen, Enlarged liver # Cirrhosis, familial ... enlarged spleen # Classic galactosemia ... enlarged liver # CMV antenatal infection ... enlarged spleen, enlarged liver # Cold antibody hemolytic anemia ... enlarged spleen # Common Variable Immunodeficiency ... enlarged spleen # Complex 1 mitochondrial respiratory chain deficiency ... enlarged liver # Complex 5 mitochondrial respiratory chain deficiency ... enlarged liver # Congenital cytomegalovirus ... enlarged spleen, enlarged liver # Congenital disorder of glycosylation type 1/IIX ... enlarged spleen, enlarged liver # Congenital disorder of glycosylation type 1A ... enlarged liver # Congenital disorder of glycosylation type 1B ... enlarged liver # Congenital disorder of glycosylation type 1H ... enlarged liver # Congenital disorder of glycosylation type 1I ... enlarged liver # Congenital disorder of glycosylation type 1K ... enlarged spleen, enlarged liver # Congenital disorder of glycosylation type 1L ... enlarged spleen, enlarged liver # Congenital disorder of glycosylation type 2E ... enlarged spleen, enlarged liver # Congenital disorder of glycosylation type 2G ... enlarged spleen, enlarged liver # Congenital hepatic fibrosis ... enlarged spleen, enlarged liver # Congenital hepatic porphyria ... enlarged liver # Congenital herpes simplex ... enlarged spleen # Congenital malaria ... enlarged spleen, enlarged liver # Congenital spherocytic anemia ... enlarged spleen # Congenital spherocytic hemolytic anemia ... enlarged spleen # Congenital syphilis ... swollen liver, enlarged spleen, enlarged liver, swollen spleen # Congenital Toxoplasmosis ... enlarged spleen, enlarged liver, enlarged liver # Congenital tuberculosis ... enlarged spleen, enlarged liver # Cooley syndrome ... enlarged spleen, enlarged liver # Cryoglobulinemia ... enlarged liver and spleen # Cyclic neutropenia ... enlarged spleen # Cystic Fibrosis ... enlarged spleen, enlarged liver # Cytomegalic Inclusion Body Disease ... Splenomegaly # Cytomegalovirus ... enlarged spleen TopD # Deafness - lymphoedema - leukemia ... enlarged spleen, enlarged liver # Deafness peripheral - neuropathy - arterial disease ... enlarged spleen # Debler anemia ... enlarged spleen, enlarged liver # Defect in synthesis of adenosylcobalamin ... enlarged liver # Di Guglielmo I - acute ... enlarged spleen, enlarged liver # Di Guglielmo I - chronic ... enlarged spleen # Dibasic aminoaciduria 2 ... enlarged spleen, enlarged liver # Diffuse neonatal hemangiomatosis ... enlarged liver # Distomatosis ... enlarged liver # Dressler (D.)syndrome ... enlarged liver # Dykes-Markes-Harper syndrome ... enlarged spleen, enlarged liver # Dyserythropoietic anemia, congenital type 1 ... enlarged spleen, enlarged liver # Dyserythropoietic anemia, congenital type 2 ... enlarged spleen, enlarged liver # Dyserythropoietic anemia, congenital type 3 ... enlarged spleen, enlarged liver # Dysplastic cortical hyperostosis ... enlarged spleen TopE # Elejalde syndrome ... enlarged liver # Emanuel syndrome ... enlarged spleen, enlarged liver # End Stage Liver Failure ... enlarged liver # Endocardial fibroelastosis ... enlarged liver # Endomyocardial fibrosis ... enlarged spleen, enlarged liver # Enterovirus antenatal infection ... enlarged liver # Epstein-Barr virus, chronic ... enlarged spleen, enlarged liver # Erdheim-Chester syndrome ... enlarged spleen, enlarged liver # Essential mixed cryoglobulinemia ... enlarged spleen # Essential thrombocytosis - same as essential thrombocythemia ... enlarged spleen TopF # Familial hyperchylomicronemia ... enlarged spleen, enlarged liver # Familial hyperlipoproteinemia ... enlarged spleen, enlarged liver # Familial hyperlipoproteinemia type 1 ... enlarged spleen, enlarged liver # Familial Mediterranean fever ... enlarged spleen # Familial myelofibrosis ... enlarged spleen, enlarged liver # Fanconi-Bickel syndrome ... enlarged liver # Farber's disease ... enlarged liver and spleen # Fascioliasis ... enlarged spleen, enlarged liver # Felty Syndrome ... enlarged spleen, enlarged liver # Fluke infections ... Hepatosplenomegaly # Forbes disease ... enlarged liver # Fructose intolerance ... enlarged liver # Fructose-1,6-bisphosphatase deficiency, hereditary ... enlarged liver # Fructose-1-phosphate aldolase deficiency, hereditary ... enlarged liver # Fucosidosis type 1 ... enlarged liver and spleen # Fucosidosis type II ... enlarged liver, enlarged liver and spleen TopG # Galactokinase deficiency ... enlarged spleen, enlarged liver # Galactosemia I ... enlarged liver # Game-Friedman-Paradice syndrome ... enlarged spleen # Gangliosidosis generalized GM1, type 1 ... enlarged liver, enlarged liver and spleen # Garret-Tripp syndrome ... enlarged spleen # Gaucher Disease ... spleen enlargement, enlarged liver and spleen # Gaucher disease type 1 ... enlarged liver and spleen # Gaucher disease type 2 ... enlarged liver and spleen # Gaucher disease type 3 ... enlarged liver and spleen # Gaucher-like disease ... enlarged spleen # Geleophysic dwarfism ... enlarged liver # Ghosal syndrome ... enlarged spleen # Glutaric Aciduria, neonatal form of type II A ... enlarged liver # Glutaricaciduria 2B ... enlarged liver # Glutaricaciduria I ... enlarged liver # Glycogen storage disease type 1C ... enlarged liver # Glycogen storage disease type 1D ... enlarged liver # Glycogen storage disease type 2 ... enlarged liver # Glycogen storage disease type 6 ... enlarged liver # Glycogen storage disease type 6A, due to phosphorylase kinase deficiency ... enlarged liver # Glycogenosis type 2 ... enlarged liver # Glycogenosis type 8 ... enlarged liver # Glycoprotein storage disease ... enlarged spleen # GM1 gangliosidosis ... enlarged liver, enlarged liver and spleen # Goldberg syndrome ... enlarged spleen, enlarged liver # Goldstein-Hutt syndrome ... enlarged spleen # Griscelli disease ... enlarged spleen, enlarged liver # Griscelli syndrome type II ... enlarged spleen, enlarged liver TopH # Hairy cell leukemia ... enlarged spleen # Hanot-MacMahon-Thannhauser syndrome ... enlarged spleen, enlarged liver # Hashimoto-Pritzker syndrome ... enlarged liver # Helminth infections ... Hepatosplenomegaly # Helminthiasis ... enlarged spleen, enlarged liver # Hemangioendothelioma ... enlarged spleen, enlarged liver # Hemochromatosis type 1 ... enlarged liver # Hemochromatosis type 2 ... enlarged liver # Hemochromatosis type 3 ... enlarged liver # Hemochromatosis type 4 ... enlarged liver # Hemoglobin E homozygous ... enlarged spleen # Hemoglobin H ... enlarged spleen, enlarged liver # Hemoglobin, constant spring ... enlarged spleen # Hemolytic anemia, lethal - genital anomalies ... enlarged spleen, enlarged liver, enlarged liver # Hemolytic uremic syndrome ... enlarged spleen, enlarged liver # Hemophagocytic lymphohistiocytosis, familial, 1 ... enlarged spleen, enlarged liver, enlarged liver # Hemophagocytic lymphohistiocytosis, familial, 2 ... enlarged spleen, enlarged liver # Hemophagocytic lymphohistiocytosis, familial, 3 ... enlarged spleen, enlarged liver # Hemophagocytic lymphohistiocytosis, familial, 4 ... enlarged spleen, enlarged liver # Hemophagocytic reticulosis ... enlarged spleen, enlarged liver # Hemorrhagic thrombocythemia ... enlarged spleen # Hepatic encephalopathy syndrome ... enlarged liver # Hepatic fibrosis, congenital ... enlarged liver # Hepatitis X (non-A,-B,-C,-D,-E) ... enlarged liver # Hepatoma ... enlarged spleen, enlarged liver # Hepatorenal tyrosinemia ... enlarged spleen, enlarged liver # Hereditary Hemochromatosis ... enlarged liver # Hereditary non-spherocytic hemolytic anemia ... enlarged spleen, enlarged liver # Hereditary spherocytic hemolytic anemia ... enlarged spleen # Hereditary spherocytosis ... enlarged spleen # Histiocytosis, Non-Langerhans-Cell ... enlarged spleen, enlarged liver # HMG CoA synthetase deficiency ... enlarged liver # Hodgkin's Disease ... enlarged spleen, enlarged liver # Hunter-Carpenter-Macdonald syndrome ... enlarged spleen, enlarged liver # Hydatidosis ... enlarged liver # Hydrops ectrodactyly syndactyly ... enlarged liver # Hydrops fetalis ... enlarged spleen, enlarged liver # Hyper-IgM Syndrome ... enlarged spleen, enlarged liver, enlarged liver # Hyperbilirubinemia ... enlarged spleen # Hypereosinophilic syndrome ... enlarged spleen, enlarged liver # Hyperimidodipeptiduria ... enlarged spleen # Hyperimmunoglobinemia D with recurrent fever ... enlarged spleen, enlarged liver # Hyperlipoproteinemia type 3 ... enlarged spleen, enlarged liver # Hyperlipoproteinemia type 5 ... enlarged spleen, enlarged liver # Hyperlysinemia, persistent ... enlarged spleen, enlarged liver # Hyperparathyroidism, neonatal severe primary ... enlarged spleen, enlarged liver # Hyperpipecolatemia ... enlarged liver # Hypoplasia hepatic ductular ... enlarged spleen, enlarged liver TopI # I cell disease ... enlarged liver, enlarged liver and spleen # Idiopathic hypereosinophilic syndrome ... enlarged spleen # Immunoproliferative diseases ... Hepatosplenomegaly # Inborn amino acid metabolism disorder ... enlarged spleen, enlarged liver, enlarged liver # Infantile multisystem inflammatory disease ... enlarged spleen, enlarged liver # Infantile Refsum Disease ... hepatomegaly (enlargement of the liver) # Infantile sialic acid storage disorder ... enlarged spleen, enlarged liver # Intrahepatic cholangiocarcinoma ... enlarged liver TopJ # Jequier-Kozlowski-skeletal dysplasia ... enlarged spleen, enlarged liver # Juvenile myelomonocytic leukemia ... enlarged spleen, enlarged liver TopK # Katayama fever ... enlarged spleen, enlarged liver # Korovnikov syndrome ... enlarged spleen TopL # Langerhans Cell Histiocytosis ... enlarged liver # Large granular lymphocyte leukemia ... enlarged spleen, enlarged liver, enlarged liver # Lathosterolosis ... enlarged spleen, enlarged liver # Leiomyosarcoma ... enlarged liver # Leishmaniasis ... enlarged spleen, enlarged liver, enlarged liver # Letterer-Siwe disease ... enlarged spleen, enlarged liver # Leukemia ... Swollen liver, Swollen spleen # Leukemia, B-cell, chronic ... enlarged spleen, enlarged liver # Leukemia, Myeloid ... enlarged spleen, enlarged liver # Leukemia, T-cell, chronic ... enlarged spleen # Lipidosis with triglyceride storage disease ... enlarged spleen, enlarged liver # Lipoamide dehydrogenase deficiency ... enlarged liver # Lissencephaly ... enlarged spleen, enlarged liver # Lissencephaly syndrome type 1 ... enlarged spleen, enlarged liver # Liver abscess ... enlarged liver # Liver cancer ... enlarged liver # Liver conditions ... Splenomegaly # Lupus ... enlarged spleen, enlarged liver # Lymph node neoplasm ... enlarged spleen # Lymphadenopathy, angioimmunoblastic with dysproteinemia ... enlarged spleen, enlarged liver, enlarged liver # Lymphoblastic lymphoma ... enlarged spleen # Lymphoma ... enlarged spleen, enlarged liver TopM # Macrosomia with lethal microphthalmia ... enlarged liver # Majeed syndrome ... enlarged spleen, enlarged liver, enlarged liver # Malaria ... Splenomegaly # Mansonella ozzardi infection ... enlarged liver # Marchiafava-Micheli disease ... enlarged spleen # Mastocytosis ... enlarged spleen, enlarged liver # Mauriac syndrome ... enlarged liver # Meadows syndrome ... enlarged liver # Melioidosis ... enlarged spleen, enlarged liver # Meningococcemia ... enlarged spleen # Mental retardation - macrocephaly - coarse facies - hypotonia ... enlarged liver # Metabolic disorders ... enlarged spleen, enlarged liver # Mevalonic aciduria ... enlarged spleen, enlarged liver # Meyenburg-Altherr-Uehlinger syndrome ... enlarged spleen, enlarged liver # Microgastria short stature diabetes ... enlarged liver # Mononucleosis ... enlarged spleen, enlarged liver # Mosquito-borne diseases ... Splenomegaly # Mosse syndrome ... enlarged spleen, enlarged liver # MPS 3 C ... enlarged liver and spleen # Mucopolysaccharidoses ... enlarged spleen, enlarged liver # Mucopolysaccharidosis type 2 Hunter syndrome- mild form ... enlarged spleen, enlarged liver and spleen # Mucopolysaccharidosis type 2 Hunter syndrome- severe form ... enlarged liver and spleen # Mucopolysaccharidosis type 6 ... enlarged liver and spleen # Mucopolysaccharidosis type 7 Sly syndrome ... enlarged liver and spleen # Mucopolysaccharidosis type I Hurler syndrome ... enlarged spleen, enlarged liver, enlarged liver and spleen # Mucopolysaccharidosis type I Hurler/Scheie syndrome ... enlarged liver and spleen # Mucopolysaccharidosis VII ... spleen enlargement # Mulibrey Nanism syndrome ... enlarged liver # Multi-centric Castleman's Disease ... enlarged spleen, enlarged liver # Multiple Myeloma ... enlarged spleen, enlarged liver # Muscle phosphoglycerate kinase deficiency ... enlarged spleen # Muscular fibrosis, multifocal - obstructed vessels ... enlarged spleen, enlarged liver # Mycobacterial infections ... Splenomegaly # Mycosis fungoides ... enlarged spleen, enlarged liver # Mycosis fungoides, familial ... enlarged spleen, enlarged liver # Myelodysplastic syndromes ... Splenomegaly, enlarged spleen # Myelofibrosis ... enlarged spleen, enlarged liver # Myelofibrosis-osteosclerosis ... enlarged spleen, enlarged liver # Myeloid splenomegaly ... enlarged spleen TopN # Nakajo-Nishimura syndrome ... enlarged spleen # Navajo neurohepatopathy ... enlarged liver # Neonatal ALD ... hepatomegaly (enlarged liver) # Neonatal hepatitis ... enlarged liver # Neonatal sepsis ... enlarged liver # Nephroblastomatosis, fetal ascites, macrosomia and Wilms tumor ... enlarged liver # Neuraminidase deficiency ... enlarged spleen, enlarged liver # Niemann-Pick disease ... spleen enlargement, enlarged liver and spleen # Niemann-Pick disease, type A ... enlarged spleen, enlarged liver # Niemann-Pick disease, type B ... enlarged spleen, enlarged liver # Non-Hodgkin's Lymphoma ... enlarged spleen, enlarged liver # Non-Hodgkin's lymphoma, during pregnancy ... enlarged spleen TopO # Okamuto Satomura syndrome ... enlarged spleen # Omenn syndrome ... enlarged spleen, enlarged liver # Omsk hemorrhagic fever ... enlarged spleen # Opisthorchiasis ... enlarged liver # Organic acidemia ... enlarged liver # Ornithine transcarbamylase (OTC) Deficiency ... enlarged liver # Orotic aciduria hereditary ... enlarged spleen # Osteopetrosis lethal ... enlarged liver and spleen # Overhydrated hereditary stomatocytosis ... enlarged spleen TopP # Periodic hyperlysinemia ... enlarged spleen, enlarged liver # Peroxisomal bifunctional enzyme deficiency ... enlarged liver # Peroxisome biogenesis disorders ... enlarged liver # PFIC ... enlarged spleen, enlarged liver # Philadelphia-negative chronic myeloid leukemia ... enlarged spleen # Plasma cell leukemia ... enlarged spleen, enlarged liver # POEMS syndrome ... enlarged spleen, enlarged liver # Polyarthritis, systemic ... enlarged spleen, enlarged liver # Polycystic kidney disease type 1 ... enlarged spleen # Polycystic kidney disease, adult type ... enlarged spleen # Polycystic kidney disease, type 2 ... enlarged spleen # Polycythemia ... enlarged spleen, enlarged liver # Polycythemia vera ... enlarged spleen # Porphyria, congenital erythropoietic ... enlarged spleen # Portal hypertension ... enlarged spleen # Portal hypertension due to intrahepatic block ... enlarged spleen # Portal thrombosis ... enlarged spleen # Portal vein thrombosis ... enlarged spleen # Postperfusion syndrome ... enlarged spleen # Primary biliary cirrhosis ... enlarged liver # Primary granulocytic sarcoma ... enlarged spleen # Primary malignant lymphoma ... enlarged spleen # Primary sclerosing cholangitis ... enlarged liver # Progeria short stature pigmented nevi ... enlarged liver # Prolidase deficiency ... enlarged spleen # Prolymphocytic leukemia ... enlarged spleen # Proximal tubulopathy - diabetes mellitus - cerebellar ataxia ... enlarged liver # Pseudo-torch syndrome ... enlarged spleen, enlarged liver # Pseudoadrenoleukodystrophy ... enlarged liver # Pulmonary valve stenosis ... enlarged liver # Pulmonary venous return anomaly ... enlarged liver # Pylephlebitis ... enlarged liver # Pyruvate carboxylase deficiency, Group A ... enlarged liver # Pyruvate Kinase Deficiency ... enlarged spleen # Pyruvate kinase deficiency, hemolytic anemia ... enlarged spleen # Pyruvate kinase deficiency, liver type ... enlarged spleen # Pyruvate kinase deficiency, muscle type ... enlarged spleen TopQ # Q fever ... enlarged spleen, enlarged liver TopR # Refsum disease, infantile form ... enlarged liver # Relapsing fever ... enlarged spleen, enlarged liver # Reticuloendotheliosis ... enlarged spleen, enlarged liver # Retinal telangiectasia and hypogammaglobulinemia ... enlarged spleen # Reye's Syndrome ... enlarged liver # Richter syndrome ... enlarged spleen, enlarged liver # Rietti-Greppi-Micheli syndrome ... enlarged spleen, enlarged liver # Right heart failure ... enlarged liver # Roifman syndrome ... enlarged spleen, enlarged liver # Rosai-Dorfman disease ... enlarged spleen, enlarged liver # Rubella congenital syndrome ... enlarged spleen, enlarged liver, Hepatosplenomegaly TopS # Sandhoff Disease ... enlarged liver and spleen # Sarrouy disease ... enlarged spleen, enlarged liver # SCARF syndrome ... enlarged liver # Schistosomiasis ... enlarged liver, hepatosplenomegaly # Schnitzler syndrome ... enlarged spleen, enlarged liver # Schridde syndrome ... enlarged spleen # Sea-Blue histiocytosis ... enlarged spleen # Secondary syphilis ... enlarged spleen # Short stature - cranial hyperostosis - hepatomegaly ... enlarged liver # Short stature, cranial hyperostosis, hepatomegaly and diabetes ... enlarged spleen, enlarged liver # Sialidosis type II ... enlarged spleen, enlarged liver # Sialidosis type II, infantile ... enlarged spleen, enlarged liver # Sialuria syndrome ... enlarged spleen, enlarged liver # Sialuria, French type ... enlarged spleen, enlarged liver # Siccardi syndrome ... enlarged spleen, enlarged liver # Sickle Cell Anemia ... enlarged spleen, enlarged liver, enlarged liver # Sideroblastic anemia, autosomal ... enlarged spleen, enlarged liver # Sideroblastic anemia, hereditary ... enlarged spleen, enlarged liver # Simpson-Golabi-Behmel syndrome, type 1 (SGBS1) ... enlarged spleen # Sitosterolemia ... enlarged spleen # Smith disease ... enlarged spleen # Soft Tissue Sarcoma ... Hepatosplenomegaly # Speech impairment ... Hepatosplenomegaly # Spherocytic hereditary elliptocytosis ... enlarged spleen # Spherocytosis ... enlarged spleen # Sphingolipidosis ... enlarged spleen, enlarged liver # Spirochetes disease ... enlarged spleen # Spleen Cancer ... abdominal masses under right and left rib cage (splenomegaly and hepatomegaly) # Spleen conditions ... Splenomegaly, Hepatosplenomegaly # Spondyloepimetaphyseal dysplasia congenita, Iraqi ... enlarged spleen, enlarged liver # Spondyloepimetaphyseal dysplasia, hypotrichosis ... enlarged spleen, enlarged liver # Spondylometaphyseal dysplasia with combined immunodeficiency ... enlarged spleen # Spotted fevers ... Hepatosplenomegaly # Spranger syndrome ... enlarged spleen, enlarged liver # Stauffer syndrome ... enlarged spleen, enlarged liver # Still's Disease, Adult-Onset ... enlarged spleen, enlarged liver # Strudwick syndrome ... enlarged spleen, enlarged liver # Stuart-Bras disease ... enlarged liver # Sulfatidosis juvenile, Austin type ... enlarged spleen, enlarged liver # Summerskill-Walshe-Tygstrup syndrome ... enlarged liver # Systemic Juvenile Rheumatoid Arthritis ... enlarged spleen, enlarged liver # Systemic mastocytosis ... enlarged spleen, enlarged liver TopT # Tang Hsi Ryu syndrome ... enlarged spleen, enlarged liver # Tangier disease ... enlarged spleen, enlarged liver # Thalassemia ... mild spleen enlargement, spleen enlargement # Thiamine responsive megaloblastic anemia syndrome ... enlarged spleen, enlarged liver # Thoraco abdominal enteric duplication ... enlarged liver # Thoracopelvic dysostosis ... enlarged spleen, enlarged liver # Thrombocythemia ... enlarged spleen # Thrombocytopenia ... enlarged spleen # Thrombocytopenic purpura, autoimmune ... enlarged spleen # Tollner-Horst-Manzke syndrome ... enlarged spleen, enlarged liver # TORCH Syndrome ... enlarged spleen, enlarged liver # Toxocariasis ... Enlarged spleen, Enlarged liver, enlarged liver # Transposition of great arteries ... enlarged liver # TRAPS (TNF-receptor-associated periodic syndrome) ... enlarged spleen # Treponema infection ... enlarged spleen # Tricuspid valve diseases ... Hepatosplenomegaly # Triglyceride storage disease with impaired long-chain fatty acid oxidation ... enlarged liver # Tularemia ... enlarged spleen, enlarged liver # Typhoid fever ... splenomegaly, enlarged liver # Tyrosinemia ... enlarged liver TopV # Valvular dysplasia of the child ... enlarged liver # Ventricular septal defect ... enlarged liver # Virus associated hemophagocytic syndrome ... Splenomegaly # Visceral leishmaniasis (kala-azar) ... enlarged spleen, enlarged liver # Vitamin A overdose ... enlarged spleen, enlarged liver # VLCAD deficiency ... Splenomegaly # Von Gierke Disease ... Enlarged liver # Von Gierke disease IA ... enlarged liver # Von Gierke disease IB ... enlarged liver TopW # WAGR Syndrome ... Splenomegaly # Waldenström Macroglobulinemia ... enlarged spleen, enlarged liver # Waldenstrom macroglobulinemia ... Splenomegaly # Wandering spleen ... Splenomegaly, enlarged spleen # Warm-reacting-antibody haemolytic anemia ... Splenomegaly # Warm-reacting-antibody hemolytic anemia ... enlarged spleen # Weber-Christian disease ... enlarged spleen # Weil syndrome ... enlarged liver # Weil's syndrome ... Splenomegaly # Weinstein Kliman Scully syndrome ... Splenomegaly # Wilson's Disease ... swollen liver, enlarged spleen, enlarged liver, swollen spleen # Wolcott-Rallison syndrome ... enlarged spleen, enlarged liver # Wolman disease ... Splenomegaly # Wolman syndrome ... enlarged spleen, enlarged liver # WT limb blood syndrome ... Splenomegaly # Wyatt disease ... enlarged liver TopX # X-linked alpha thalassemia mental retardation syndrome (ATR-X) ... Splenomegaly # X-linked lymphoproliferative syndrome ... Splenomegaly, enlarged spleen, enlarged liver # X-linked sideroblastic anemia ... Splenomegaly, enlarged spleen, enlarged liver # Xerocytosis, heriditary ... Hepatosplenomegaly TopZ # ZAP70 deficiency ... Splenomegaly # Zellweger Syndrome ... enlarged liver # Zellweger-like syndrome, without peroxisomal anomalies ... enlarged liver # Zimmerman-Laband syndrome ... Splenomegaly, enlarged spleen, enlarged liver TopConditions listing medical complications: Enlarged liver and spleen: The following list of medical conditions have 'Enlarged liver and spleen' or similar listed as a medical complication in our database. This computer-generated list of complications may be inaccurate or incomplete. Always seek prompt professional medical advice about the cause of any symptom. TopB # Biliary atresia, intrahepatic, non syndromic form ... enlarged spleen # Biliary atresia, intrahepatic, syndromic form ... enlarged spleen TopH # Hemochromatosis ... enlarged liver # Hereditary hemorrhagic telangiectasia ... enlarged liver TopI # Infantile sialic acid storage disorder ... enlarged spleen, enlarged liver # Infectious myocarditis ... enlarged liver TopM # Malaria ... enlarged spleen, enlarged liver TopP # Portal hypertension ... enlarged spleen TopS # Sickle Cell Anemia ... spleen enlargement ==External links== * {{GPnotebook|1516961800}} * {{Medcyclopaedia|vii/h/HEPATOSPLENOMEGALY}} [[Category:Medical signs]] [[Category:Hepatology]] {{med-sign-stub}} {{Digestive system and abdomen symptoms and signs}} [[cs:Hepatosplenomegalie]] [[de:Hepatosplenomegalie]] [[fr:Hépatosplénomégalie]] [[pl:Hepatosplenomegalia]] [[pt:Hepatoesplenomegalia]]