Hepatosplenomegaly
1018486
225975144
2008-07-16T08:01:15Z
Thijs!bot
1392310
robot Adding: [[cs:Hepatosplenomegalie]]
{{DiseaseDisorder infobox |
Name = Hepatosplenomegaly |
ICD10 = {{ICD10|R|16|2|r|10}} |
ICD9 = {{ICD9|571.8}}, {{ICD9|789.1}}, {{ICD9|789.2}} |
ICDO = |
Image = |
Caption = |
OMIM = |
MedlinePlus = 003275 |
eMedicineSubj = |
eMedicineTopic = |
DiseasesDB = |
}}
'''Hepatosplenomegaly''' is the simultaneous enlargement of both the [[liver]] ([[hepatomegaly]]) and the [[spleen]] ([[splenomegaly]]).
==Differential diagnosis==
{{Expand list}}
#
A
# Aagenaes syndrome ... enlarged liver
# Acanthocytosis ... enlarged spleen, enlarged liver
# Acidemia, methylmalonic ... enlarged liver
# Acquired idiopathic sideroblastic anaemia ... enlarged spleen, enlarged liver
# Acquired total lipodystrophy ... enlarged liver
# Acral dysostosis - dyserythropoiesis ... enlarged spleen, enlarged liver
# Acromegaly ... enlarged spleen, enlarged liver
# Actinomycetales infection ... enlarged spleen, enlarged liver
# Acute biphenotypic leukemia ... enlarged spleen, enlarged liver
# Acute cholinergic dysautonomia ... enlarged spleen, enlarged liver
# Acute leukaemia of ambiguous lineage ... enlarged spleen, enlarged liver
# Acute lymphoblastic leukemia ... enlarged spleen, enlarged liver
# Acute lymphoblastic leukemia, adult ... enlarged spleen, enlarged liver
# Acute megacaryoblastic leukemia ... enlarged spleen, enlarged liver
# Acute myeloblastic leukemia type 1 ... enlarged spleen, enlarged liver, enlarged liver
# Acute myeloblastic leukemia type 2 ... enlarged spleen, enlarged liver
# Acute myeloblastic leukemia type 3 ... enlarged spleen, enlarged liver
# Acute myeloblastic leukemia type 4 ... enlarged spleen, enlarged liver
# Acute myeloblastic leukemia type 5 ... enlarged spleen, enlarged liver
# Acute myeloblastic leukemia type 6 ... enlarged spleen, enlarged liver
# Acute myeloblastic leukemia type 7 ... enlarged spleen, enlarged liver
# Acute myelocytic leukemia ... enlarged spleen, enlarged liver, enlarged liver, enlarged liver
# Acute myelofibrosis ... enlarged spleen, enlarged liver
# Acute myeloid leukaemia and myelodysplastic syndromes related to alkylating agent ... enlarged spleen, enlarged liver
# Acute myeloid leukaemia and myelodysplastic syndromes related to topoisomerase type II inhibitor ... enlarged spleen, enlarged liver
# Acute myeloid leukaemia and myelodysplastic syndromes, therapy related ... enlarged spleen, enlarged liver
# Acute myeloid leukemia ... enlarged spleen, enlarged liver
# Acute myeloid leukemia, adult ... enlarged spleen, enlarged liver
# Acute myelosclerosis ... enlarged spleen
# Acute panmyelosis ... enlarged spleen, enlarged liver
# Acute vitamin A toxicity ... enlarged liver
# Addison-Gull syndrome ... enlarged spleen, enlarged liver
# Adrenoleukodystrophy ... enlarged liver
# Adrenoleukodystrophy, autosomal, neonatal form ... enlarged liver
# Adult onset Still's disease ... enlarged spleen, enlarged liver
# African Sleeping sickness ... enlarged spleen
# Aggressive NK-cell leukaemia ... enlarged spleen, enlarged liver
# Aggressive systemic mastocytosis ... enlarged spleen, enlarged liver
# Aicardi-Goutieres syndrome 1 ... enlarged spleen, enlarged liver
# Aicardi-Goutieres syndrome 2 ... enlarged spleen, enlarged liver
# Aicardi-Goutieres syndrome 3 ... enlarged spleen, enlarged liver
# Aicardi-Goutieres syndrome 4 ... enlarged spleen, enlarged liver
# Aicardi-Goutieres syndrome 5 ... enlarged spleen, enlarged liver
# Alagille Syndrome ... enlarged spleen, enlarged liver
# Albers-Schonberg disease - malignant recessive form ... enlarged spleen, enlarged liver, enlarged liver
# Alcohol-induced pseudo-Cushing syndrome ... enlarged liver
# Aldolase A deficiency ... enlarged spleen, enlarged liver
# ALL-Down syndrome ... enlarged spleen, enlarged liver
# Alpha-mannosidosis type II ... enlarged liver
# Amyloidosis ... enlarged spleen, enlarged liver
# Amyloidosis, familial visceral ... enlarged spleen, enlarged liver
# Andersen disease ... enlarged spleen, enlarged liver, enlarged liver
# Anemia, hypochromic microcytic ... enlarged spleen
# Anemia, Neonatal ... enlarged spleen, enlarged liver
# Anemia, Sideroblastic ... enlarged spleen, enlarged liver
# Angioimmunoblastic with dysproteinemia lymphadenopathy ... enlarged liver and spleen
# Angiosarcoma of the liver ... enlarged liver
# Apo A-I deficiency ... enlarged spleen
# Arakawa's syndrome 2 ... enlarged spleen, enlarged liver
# AREDYLD ... enlarged liver
# Arginase deficiency ... enlarged liver
# Argininosuccinase lyase deficiency, neonatal ... enlarged liver
# Argininosuccinic aciduria ... enlarged liver
# Arthralgia - purpura - weakness syndrome ... enlarged spleen
# Aspartylglycosaminuria ... enlarged spleen, enlarged liver
# Asrar-Facharzt-Haque syndrome ... enlarged spleen, enlarged liver
# Athabaskan severe combined immunodeficiency ... enlarged liver
# Autoimmune Hepatitis ... enlarged liver
# Autoimmune Lymphoproliferative Syndrome ... enlarged spleen, enlarged liver
# Autoimmune Thrombocytopenia ... enlarged spleen
TopB
# Baker-Winegrad disease ... enlarged liver
# Ballard syndrome ... enlarged spleen, enlarged liver
# Banti's syndrome ... enlarged spleen, enlarged liver, enlarged liver
# Bantu siderosis ... enlarged liver
# Bartonella ... enlarged liver
# Bartonellosis ... enlarged spleen, enlarged liver
# Bearn-Kunkel syndrome ... enlarged spleen, enlarged liver
# Benign intrahepatic cholestasis type 1 ... enlarged liver
# Benign intrahepatic cholestasis type 2 ... enlarged liver
# Berardinelli-Seip congenital lipodystrophy ... enlarged liver
# Berardinelli-Seip congenital lipodystrophy, type 1 ... enlarged liver
# Berardinelli-Seip congenital lipodystrophy, type 2 ... enlarged liver
# Bernheim's syndrome ... enlarged liver
# Besnier-Boeck-Schaumann disease ... enlarged spleen, enlarged liver
# Bile acid synthesis defects ... enlarged spleen, enlarged liver
# Bile acid synthesis defects, congenital, 1 ... enlarged spleen, enlarged liver
# Bile acid synthesis defects, congenital, 2 ... enlarged spleen, enlarged liver
# Bile acid synthesis defects, congenital, 3 ... enlarged spleen, enlarged liver
# Bile acid synthesis defects, congenital, 4 ... enlarged spleen, enlarged liver
# Bile Duct Cancer ... Enlarged liver
# Bile Duct Conditions ... Enlarged liver
# Bile plug syndrome ... enlarged liver
# Biliary Atresia ... enlarged liver
# Biliary atresia, intrahepatic, non syndromic form ... enlarged liver
# Biliary atresia, intrahepatic, syndromic form ... enlarged liver
# Biliary disorder ... Enlarged liver
# Biliary hypoplasia ... enlarged liver
# Blastoma ... enlarged spleen, enlarged liver
# Brucellosis ... enlarged spleen, enlarged liver, enlarged liver
# Brunzell syndrome ... enlarged spleen, enlarged liver
# Budd-Chiari syndrome ... enlarged spleen, enlarged liver, enlarged liver
TopC
# Camurati-Engelmann Disease ... enlarged liver and spleen
# Carbamoyl-phosphate synthase 1 deficiency ... enlarged liver
# Carcinoid syndrome ... enlarged liver
# Cardiomyopathy - hypogonadism - metabolic anomalies ... enlarged liver
# Cardiomyopathy - spherocytosis ... enlarged spleen, enlarged liver
# Cardiomyopathy due to anthracyclines ... enlarged liver
# Carnitine palmitoyl transferase 1 deficiency ... enlarged liver
# Carnitine palmitoyl transferase 2 deficiency ... enlarged liver
# Carnitine palmitoyl transferase deficiency ... enlarged liver
# Carnitine palmitoyl transferase II deficiency, infantile hepatocardiomuscular type ... enlarged liver
# Carnitine-acylcarnitine translocase deficiency ... enlarged liver
# Caroli Disease ... enlarged liver
# Caspase-8 deficiency ... enlarged spleen
# Castellani syndrome ... enlarged spleen, enlarged liver
# CCF ... enlarged liver
# CDG syndrome (generic term) ... enlarged spleen, enlarged liver
# Cerebrorenodigital syndrome ... enlarged spleen
# Chédiak-Higashi syndrome ... enlarged liver
# Chagas disease ... enlarged spleen, enlarged liver, Hepatosplenomegaly
# Cholestasis, progressive familial intrahepatic 1 ... enlarged spleen, enlarged liver
# Cholestasis, progressive familial intrahepatic 2 ... enlarged spleen, enlarged liver
# Cholestasis, progressive familial intrahepatic 3 ... enlarged spleen, enlarged liver
# Choriocarcinoma, infantile ... enlarged liver
# Chronic Fatigue Syndrome ... enlarged liver
# Chronic Granulomatous Disease ... enlarged spleen, enlarged liver, enlarged liver
# Chronic Hepatitis C ... Enlarged spleen, Enlarged liver
# Chronic lymphocytic leukemia ... enlarged spleen
# Chronic myelogenous leukemia ... enlarged spleen
# Chronic myelomonocytic leukemia ... enlarged spleen, enlarged liver
# Chronic Myeloproliferative Disorders ... enlarged spleen
# Chronic vitamin A toxicity ... enlarged liver
# Cirrhosis of the liver ... Enlarged spleen, Enlarged liver
# Cirrhosis, familial ... enlarged spleen
# Classic galactosemia ... enlarged liver
# CMV antenatal infection ... enlarged spleen, enlarged liver
# Cold antibody hemolytic anemia ... enlarged spleen
# Common Variable Immunodeficiency ... enlarged spleen
# Complex 1 mitochondrial respiratory chain deficiency ... enlarged liver
# Complex 5 mitochondrial respiratory chain deficiency ... enlarged liver
# Congenital cytomegalovirus ... enlarged spleen, enlarged liver
# Congenital disorder of glycosylation type 1/IIX ... enlarged spleen, enlarged liver
# Congenital disorder of glycosylation type 1A ... enlarged liver
# Congenital disorder of glycosylation type 1B ... enlarged liver
# Congenital disorder of glycosylation type 1H ... enlarged liver
# Congenital disorder of glycosylation type 1I ... enlarged liver
# Congenital disorder of glycosylation type 1K ... enlarged spleen, enlarged liver
# Congenital disorder of glycosylation type 1L ... enlarged spleen, enlarged liver
# Congenital disorder of glycosylation type 2E ... enlarged spleen, enlarged liver
# Congenital disorder of glycosylation type 2G ... enlarged spleen, enlarged liver
# Congenital hepatic fibrosis ... enlarged spleen, enlarged liver
# Congenital hepatic porphyria ... enlarged liver
# Congenital herpes simplex ... enlarged spleen
# Congenital malaria ... enlarged spleen, enlarged liver
# Congenital spherocytic anemia ... enlarged spleen
# Congenital spherocytic hemolytic anemia ... enlarged spleen
# Congenital syphilis ... swollen liver, enlarged spleen, enlarged liver, swollen spleen
# Congenital Toxoplasmosis ... enlarged spleen, enlarged liver, enlarged liver
# Congenital tuberculosis ... enlarged spleen, enlarged liver
# Cooley syndrome ... enlarged spleen, enlarged liver
# Cryoglobulinemia ... enlarged liver and spleen
# Cyclic neutropenia ... enlarged spleen
# Cystic Fibrosis ... enlarged spleen, enlarged liver
# Cytomegalic Inclusion Body Disease ... Splenomegaly
# Cytomegalovirus ... enlarged spleen
TopD
# Deafness - lymphoedema - leukemia ... enlarged spleen, enlarged liver
# Deafness peripheral - neuropathy - arterial disease ... enlarged spleen
# Debler anemia ... enlarged spleen, enlarged liver
# Defect in synthesis of adenosylcobalamin ... enlarged liver
# Di Guglielmo I - acute ... enlarged spleen, enlarged liver
# Di Guglielmo I - chronic ... enlarged spleen
# Dibasic aminoaciduria 2 ... enlarged spleen, enlarged liver
# Diffuse neonatal hemangiomatosis ... enlarged liver
# Distomatosis ... enlarged liver
# Dressler (D.)syndrome ... enlarged liver
# Dykes-Markes-Harper syndrome ... enlarged spleen, enlarged liver
# Dyserythropoietic anemia, congenital type 1 ... enlarged spleen, enlarged liver
# Dyserythropoietic anemia, congenital type 2 ... enlarged spleen, enlarged liver
# Dyserythropoietic anemia, congenital type 3 ... enlarged spleen, enlarged liver
# Dysplastic cortical hyperostosis ... enlarged spleen
TopE
# Elejalde syndrome ... enlarged liver
# Emanuel syndrome ... enlarged spleen, enlarged liver
# End Stage Liver Failure ... enlarged liver
# Endocardial fibroelastosis ... enlarged liver
# Endomyocardial fibrosis ... enlarged spleen, enlarged liver
# Enterovirus antenatal infection ... enlarged liver
# Epstein-Barr virus, chronic ... enlarged spleen, enlarged liver
# Erdheim-Chester syndrome ... enlarged spleen, enlarged liver
# Essential mixed cryoglobulinemia ... enlarged spleen
# Essential thrombocytosis - same as essential thrombocythemia ... enlarged spleen
TopF
# Familial hyperchylomicronemia ... enlarged spleen, enlarged liver
# Familial hyperlipoproteinemia ... enlarged spleen, enlarged liver
# Familial hyperlipoproteinemia type 1 ... enlarged spleen, enlarged liver
# Familial Mediterranean fever ... enlarged spleen
# Familial myelofibrosis ... enlarged spleen, enlarged liver
# Fanconi-Bickel syndrome ... enlarged liver
# Farber's disease ... enlarged liver and spleen
# Fascioliasis ... enlarged spleen, enlarged liver
# Felty Syndrome ... enlarged spleen, enlarged liver
# Fluke infections ... Hepatosplenomegaly
# Forbes disease ... enlarged liver
# Fructose intolerance ... enlarged liver
# Fructose-1,6-bisphosphatase deficiency, hereditary ... enlarged liver
# Fructose-1-phosphate aldolase deficiency, hereditary ... enlarged liver
# Fucosidosis type 1 ... enlarged liver and spleen
# Fucosidosis type II ... enlarged liver, enlarged liver and spleen
TopG
# Galactokinase deficiency ... enlarged spleen, enlarged liver
# Galactosemia I ... enlarged liver
# Game-Friedman-Paradice syndrome ... enlarged spleen
# Gangliosidosis generalized GM1, type 1 ... enlarged liver, enlarged liver and spleen
# Garret-Tripp syndrome ... enlarged spleen
# Gaucher Disease ... spleen enlargement, enlarged liver and spleen
# Gaucher disease type 1 ... enlarged liver and spleen
# Gaucher disease type 2 ... enlarged liver and spleen
# Gaucher disease type 3 ... enlarged liver and spleen
# Gaucher-like disease ... enlarged spleen
# Geleophysic dwarfism ... enlarged liver
# Ghosal syndrome ... enlarged spleen
# Glutaric Aciduria, neonatal form of type II A ... enlarged liver
# Glutaricaciduria 2B ... enlarged liver
# Glutaricaciduria I ... enlarged liver
# Glycogen storage disease type 1C ... enlarged liver
# Glycogen storage disease type 1D ... enlarged liver
# Glycogen storage disease type 2 ... enlarged liver
# Glycogen storage disease type 6 ... enlarged liver
# Glycogen storage disease type 6A, due to phosphorylase kinase deficiency ... enlarged liver
# Glycogenosis type 2 ... enlarged liver
# Glycogenosis type 8 ... enlarged liver
# Glycoprotein storage disease ... enlarged spleen
# GM1 gangliosidosis ... enlarged liver, enlarged liver and spleen
# Goldberg syndrome ... enlarged spleen, enlarged liver
# Goldstein-Hutt syndrome ... enlarged spleen
# Griscelli disease ... enlarged spleen, enlarged liver
# Griscelli syndrome type II ... enlarged spleen, enlarged liver
TopH
# Hairy cell leukemia ... enlarged spleen
# Hanot-MacMahon-Thannhauser syndrome ... enlarged spleen, enlarged liver
# Hashimoto-Pritzker syndrome ... enlarged liver
# Helminth infections ... Hepatosplenomegaly
# Helminthiasis ... enlarged spleen, enlarged liver
# Hemangioendothelioma ... enlarged spleen, enlarged liver
# Hemochromatosis type 1 ... enlarged liver
# Hemochromatosis type 2 ... enlarged liver
# Hemochromatosis type 3 ... enlarged liver
# Hemochromatosis type 4 ... enlarged liver
# Hemoglobin E homozygous ... enlarged spleen
# Hemoglobin H ... enlarged spleen, enlarged liver
# Hemoglobin, constant spring ... enlarged spleen
# Hemolytic anemia, lethal - genital anomalies ... enlarged spleen, enlarged liver, enlarged liver
# Hemolytic uremic syndrome ... enlarged spleen, enlarged liver
# Hemophagocytic lymphohistiocytosis, familial, 1 ... enlarged spleen, enlarged liver, enlarged liver
# Hemophagocytic lymphohistiocytosis, familial, 2 ... enlarged spleen, enlarged liver
# Hemophagocytic lymphohistiocytosis, familial, 3 ... enlarged spleen, enlarged liver
# Hemophagocytic lymphohistiocytosis, familial, 4 ... enlarged spleen, enlarged liver
# Hemophagocytic reticulosis ... enlarged spleen, enlarged liver
# Hemorrhagic thrombocythemia ... enlarged spleen
# Hepatic encephalopathy syndrome ... enlarged liver
# Hepatic fibrosis, congenital ... enlarged liver
# Hepatitis X (non-A,-B,-C,-D,-E) ... enlarged liver
# Hepatoma ... enlarged spleen, enlarged liver
# Hepatorenal tyrosinemia ... enlarged spleen, enlarged liver
# Hereditary Hemochromatosis ... enlarged liver
# Hereditary non-spherocytic hemolytic anemia ... enlarged spleen, enlarged liver
# Hereditary spherocytic hemolytic anemia ... enlarged spleen
# Hereditary spherocytosis ... enlarged spleen
# Histiocytosis, Non-Langerhans-Cell ... enlarged spleen, enlarged liver
# HMG CoA synthetase deficiency ... enlarged liver
# Hodgkin's Disease ... enlarged spleen, enlarged liver
# Hunter-Carpenter-Macdonald syndrome ... enlarged spleen, enlarged liver
# Hydatidosis ... enlarged liver
# Hydrops ectrodactyly syndactyly ... enlarged liver
# Hydrops fetalis ... enlarged spleen, enlarged liver
# Hyper-IgM Syndrome ... enlarged spleen, enlarged liver, enlarged liver
# Hyperbilirubinemia ... enlarged spleen
# Hypereosinophilic syndrome ... enlarged spleen, enlarged liver
# Hyperimidodipeptiduria ... enlarged spleen
# Hyperimmunoglobinemia D with recurrent fever ... enlarged spleen, enlarged liver
# Hyperlipoproteinemia type 3 ... enlarged spleen, enlarged liver
# Hyperlipoproteinemia type 5 ... enlarged spleen, enlarged liver
# Hyperlysinemia, persistent ... enlarged spleen, enlarged liver
# Hyperparathyroidism, neonatal severe primary ... enlarged spleen, enlarged liver
# Hyperpipecolatemia ... enlarged liver
# Hypoplasia hepatic ductular ... enlarged spleen, enlarged liver
TopI
# I cell disease ... enlarged liver, enlarged liver and spleen
# Idiopathic hypereosinophilic syndrome ... enlarged spleen
# Immunoproliferative diseases ... Hepatosplenomegaly
# Inborn amino acid metabolism disorder ... enlarged spleen, enlarged liver, enlarged liver
# Infantile multisystem inflammatory disease ... enlarged spleen, enlarged liver
# Infantile Refsum Disease ... hepatomegaly (enlargement of the liver)
# Infantile sialic acid storage disorder ... enlarged spleen, enlarged liver
# Intrahepatic cholangiocarcinoma ... enlarged liver
TopJ
# Jequier-Kozlowski-skeletal dysplasia ... enlarged spleen, enlarged liver
# Juvenile myelomonocytic leukemia ... enlarged spleen, enlarged liver
TopK
# Katayama fever ... enlarged spleen, enlarged liver
# Korovnikov syndrome ... enlarged spleen
TopL
# Langerhans Cell Histiocytosis ... enlarged liver
# Large granular lymphocyte leukemia ... enlarged spleen, enlarged liver, enlarged liver
# Lathosterolosis ... enlarged spleen, enlarged liver
# Leiomyosarcoma ... enlarged liver
# Leishmaniasis ... enlarged spleen, enlarged liver, enlarged liver
# Letterer-Siwe disease ... enlarged spleen, enlarged liver
# Leukemia ... Swollen liver, Swollen spleen
# Leukemia, B-cell, chronic ... enlarged spleen, enlarged liver
# Leukemia, Myeloid ... enlarged spleen, enlarged liver
# Leukemia, T-cell, chronic ... enlarged spleen
# Lipidosis with triglyceride storage disease ... enlarged spleen, enlarged liver
# Lipoamide dehydrogenase deficiency ... enlarged liver
# Lissencephaly ... enlarged spleen, enlarged liver
# Lissencephaly syndrome type 1 ... enlarged spleen, enlarged liver
# Liver abscess ... enlarged liver
# Liver cancer ... enlarged liver
# Liver conditions ... Splenomegaly
# Lupus ... enlarged spleen, enlarged liver
# Lymph node neoplasm ... enlarged spleen
# Lymphadenopathy, angioimmunoblastic with dysproteinemia ... enlarged spleen, enlarged liver, enlarged liver
# Lymphoblastic lymphoma ... enlarged spleen
# Lymphoma ... enlarged spleen, enlarged liver
TopM
# Macrosomia with lethal microphthalmia ... enlarged liver
# Majeed syndrome ... enlarged spleen, enlarged liver, enlarged liver
# Malaria ... Splenomegaly
# Mansonella ozzardi infection ... enlarged liver
# Marchiafava-Micheli disease ... enlarged spleen
# Mastocytosis ... enlarged spleen, enlarged liver
# Mauriac syndrome ... enlarged liver
# Meadows syndrome ... enlarged liver
# Melioidosis ... enlarged spleen, enlarged liver
# Meningococcemia ... enlarged spleen
# Mental retardation - macrocephaly - coarse facies - hypotonia ... enlarged liver
# Metabolic disorders ... enlarged spleen, enlarged liver
# Mevalonic aciduria ... enlarged spleen, enlarged liver
# Meyenburg-Altherr-Uehlinger syndrome ... enlarged spleen, enlarged liver
# Microgastria short stature diabetes ... enlarged liver
# Mononucleosis ... enlarged spleen, enlarged liver
# Mosquito-borne diseases ... Splenomegaly
# Mosse syndrome ... enlarged spleen, enlarged liver
# MPS 3 C ... enlarged liver and spleen
# Mucopolysaccharidoses ... enlarged spleen, enlarged liver
# Mucopolysaccharidosis type 2 Hunter syndrome- mild form ... enlarged spleen, enlarged liver and spleen
# Mucopolysaccharidosis type 2 Hunter syndrome- severe form ... enlarged liver and spleen
# Mucopolysaccharidosis type 6 ... enlarged liver and spleen
# Mucopolysaccharidosis type 7 Sly syndrome ... enlarged liver and spleen
# Mucopolysaccharidosis type I Hurler syndrome ... enlarged spleen, enlarged liver, enlarged liver and spleen
# Mucopolysaccharidosis type I Hurler/Scheie syndrome ... enlarged liver and spleen
# Mucopolysaccharidosis VII ... spleen enlargement
# Mulibrey Nanism syndrome ... enlarged liver
# Multi-centric Castleman's Disease ... enlarged spleen, enlarged liver
# Multiple Myeloma ... enlarged spleen, enlarged liver
# Muscle phosphoglycerate kinase deficiency ... enlarged spleen
# Muscular fibrosis, multifocal - obstructed vessels ... enlarged spleen, enlarged liver
# Mycobacterial infections ... Splenomegaly
# Mycosis fungoides ... enlarged spleen, enlarged liver
# Mycosis fungoides, familial ... enlarged spleen, enlarged liver
# Myelodysplastic syndromes ... Splenomegaly, enlarged spleen
# Myelofibrosis ... enlarged spleen, enlarged liver
# Myelofibrosis-osteosclerosis ... enlarged spleen, enlarged liver
# Myeloid splenomegaly ... enlarged spleen
TopN
# Nakajo-Nishimura syndrome ... enlarged spleen
# Navajo neurohepatopathy ... enlarged liver
# Neonatal ALD ... hepatomegaly (enlarged liver)
# Neonatal hepatitis ... enlarged liver
# Neonatal sepsis ... enlarged liver
# Nephroblastomatosis, fetal ascites, macrosomia and Wilms tumor ... enlarged liver
# Neuraminidase deficiency ... enlarged spleen, enlarged liver
# Niemann-Pick disease ... spleen enlargement, enlarged liver and spleen
# Niemann-Pick disease, type A ... enlarged spleen, enlarged liver
# Niemann-Pick disease, type B ... enlarged spleen, enlarged liver
# Non-Hodgkin's Lymphoma ... enlarged spleen, enlarged liver
# Non-Hodgkin's lymphoma, during pregnancy ... enlarged spleen
TopO
# Okamuto Satomura syndrome ... enlarged spleen
# Omenn syndrome ... enlarged spleen, enlarged liver
# Omsk hemorrhagic fever ... enlarged spleen
# Opisthorchiasis ... enlarged liver
# Organic acidemia ... enlarged liver
# Ornithine transcarbamylase (OTC) Deficiency ... enlarged liver
# Orotic aciduria hereditary ... enlarged spleen
# Osteopetrosis lethal ... enlarged liver and spleen
# Overhydrated hereditary stomatocytosis ... enlarged spleen
TopP
# Periodic hyperlysinemia ... enlarged spleen, enlarged liver
# Peroxisomal bifunctional enzyme deficiency ... enlarged liver
# Peroxisome biogenesis disorders ... enlarged liver
# PFIC ... enlarged spleen, enlarged liver
# Philadelphia-negative chronic myeloid leukemia ... enlarged spleen
# Plasma cell leukemia ... enlarged spleen, enlarged liver
# POEMS syndrome ... enlarged spleen, enlarged liver
# Polyarthritis, systemic ... enlarged spleen, enlarged liver
# Polycystic kidney disease type 1 ... enlarged spleen
# Polycystic kidney disease, adult type ... enlarged spleen
# Polycystic kidney disease, type 2 ... enlarged spleen
# Polycythemia ... enlarged spleen, enlarged liver
# Polycythemia vera ... enlarged spleen
# Porphyria, congenital erythropoietic ... enlarged spleen
# Portal hypertension ... enlarged spleen
# Portal hypertension due to intrahepatic block ... enlarged spleen
# Portal thrombosis ... enlarged spleen
# Portal vein thrombosis ... enlarged spleen
# Postperfusion syndrome ... enlarged spleen
# Primary biliary cirrhosis ... enlarged liver
# Primary granulocytic sarcoma ... enlarged spleen
# Primary malignant lymphoma ... enlarged spleen
# Primary sclerosing cholangitis ... enlarged liver
# Progeria short stature pigmented nevi ... enlarged liver
# Prolidase deficiency ... enlarged spleen
# Prolymphocytic leukemia ... enlarged spleen
# Proximal tubulopathy - diabetes mellitus - cerebellar ataxia ... enlarged liver
# Pseudo-torch syndrome ... enlarged spleen, enlarged liver
# Pseudoadrenoleukodystrophy ... enlarged liver
# Pulmonary valve stenosis ... enlarged liver
# Pulmonary venous return anomaly ... enlarged liver
# Pylephlebitis ... enlarged liver
# Pyruvate carboxylase deficiency, Group A ... enlarged liver
# Pyruvate Kinase Deficiency ... enlarged spleen
# Pyruvate kinase deficiency, hemolytic anemia ... enlarged spleen
# Pyruvate kinase deficiency, liver type ... enlarged spleen
# Pyruvate kinase deficiency, muscle type ... enlarged spleen
TopQ
# Q fever ... enlarged spleen, enlarged liver
TopR
# Refsum disease, infantile form ... enlarged liver
# Relapsing fever ... enlarged spleen, enlarged liver
# Reticuloendotheliosis ... enlarged spleen, enlarged liver
# Retinal telangiectasia and hypogammaglobulinemia ... enlarged spleen
# Reye's Syndrome ... enlarged liver
# Richter syndrome ... enlarged spleen, enlarged liver
# Rietti-Greppi-Micheli syndrome ... enlarged spleen, enlarged liver
# Right heart failure ... enlarged liver
# Roifman syndrome ... enlarged spleen, enlarged liver
# Rosai-Dorfman disease ... enlarged spleen, enlarged liver
# Rubella congenital syndrome ... enlarged spleen, enlarged liver, Hepatosplenomegaly
TopS
# Sandhoff Disease ... enlarged liver and spleen
# Sarrouy disease ... enlarged spleen, enlarged liver
# SCARF syndrome ... enlarged liver
# Schistosomiasis ... enlarged liver, hepatosplenomegaly
# Schnitzler syndrome ... enlarged spleen, enlarged liver
# Schridde syndrome ... enlarged spleen
# Sea-Blue histiocytosis ... enlarged spleen
# Secondary syphilis ... enlarged spleen
# Short stature - cranial hyperostosis - hepatomegaly ... enlarged liver
# Short stature, cranial hyperostosis, hepatomegaly and diabetes ... enlarged spleen, enlarged liver
# Sialidosis type II ... enlarged spleen, enlarged liver
# Sialidosis type II, infantile ... enlarged spleen, enlarged liver
# Sialuria syndrome ... enlarged spleen, enlarged liver
# Sialuria, French type ... enlarged spleen, enlarged liver
# Siccardi syndrome ... enlarged spleen, enlarged liver
# Sickle Cell Anemia ... enlarged spleen, enlarged liver, enlarged liver
# Sideroblastic anemia, autosomal ... enlarged spleen, enlarged liver
# Sideroblastic anemia, hereditary ... enlarged spleen, enlarged liver
# Simpson-Golabi-Behmel syndrome, type 1 (SGBS1) ... enlarged spleen
# Sitosterolemia ... enlarged spleen
# Smith disease ... enlarged spleen
# Soft Tissue Sarcoma ... Hepatosplenomegaly
# Speech impairment ... Hepatosplenomegaly
# Spherocytic hereditary elliptocytosis ... enlarged spleen
# Spherocytosis ... enlarged spleen
# Sphingolipidosis ... enlarged spleen, enlarged liver
# Spirochetes disease ... enlarged spleen
# Spleen Cancer ... abdominal masses under right and left rib cage (splenomegaly and hepatomegaly)
# Spleen conditions ... Splenomegaly, Hepatosplenomegaly
# Spondyloepimetaphyseal dysplasia congenita, Iraqi ... enlarged spleen, enlarged liver
# Spondyloepimetaphyseal dysplasia, hypotrichosis ... enlarged spleen, enlarged liver
# Spondylometaphyseal dysplasia with combined immunodeficiency ... enlarged spleen
# Spotted fevers ... Hepatosplenomegaly
# Spranger syndrome ... enlarged spleen, enlarged liver
# Stauffer syndrome ... enlarged spleen, enlarged liver
# Still's Disease, Adult-Onset ... enlarged spleen, enlarged liver
# Strudwick syndrome ... enlarged spleen, enlarged liver
# Stuart-Bras disease ... enlarged liver
# Sulfatidosis juvenile, Austin type ... enlarged spleen, enlarged liver
# Summerskill-Walshe-Tygstrup syndrome ... enlarged liver
# Systemic Juvenile Rheumatoid Arthritis ... enlarged spleen, enlarged liver
# Systemic mastocytosis ... enlarged spleen, enlarged liver
TopT
# Tang Hsi Ryu syndrome ... enlarged spleen, enlarged liver
# Tangier disease ... enlarged spleen, enlarged liver
# Thalassemia ... mild spleen enlargement, spleen enlargement
# Thiamine responsive megaloblastic anemia syndrome ... enlarged spleen, enlarged liver
# Thoraco abdominal enteric duplication ... enlarged liver
# Thoracopelvic dysostosis ... enlarged spleen, enlarged liver
# Thrombocythemia ... enlarged spleen
# Thrombocytopenia ... enlarged spleen
# Thrombocytopenic purpura, autoimmune ... enlarged spleen
# Tollner-Horst-Manzke syndrome ... enlarged spleen, enlarged liver
# TORCH Syndrome ... enlarged spleen, enlarged liver
# Toxocariasis ... Enlarged spleen, Enlarged liver, enlarged liver
# Transposition of great arteries ... enlarged liver
# TRAPS (TNF-receptor-associated periodic syndrome) ... enlarged spleen
# Treponema infection ... enlarged spleen
# Tricuspid valve diseases ... Hepatosplenomegaly
# Triglyceride storage disease with impaired long-chain fatty acid oxidation ... enlarged liver
# Tularemia ... enlarged spleen, enlarged liver
# Typhoid fever ... splenomegaly, enlarged liver
# Tyrosinemia ... enlarged liver
TopV
# Valvular dysplasia of the child ... enlarged liver
# Ventricular septal defect ... enlarged liver
# Virus associated hemophagocytic syndrome ... Splenomegaly
# Visceral leishmaniasis (kala-azar) ... enlarged spleen, enlarged liver
# Vitamin A overdose ... enlarged spleen, enlarged liver
# VLCAD deficiency ... Splenomegaly
# Von Gierke Disease ... Enlarged liver
# Von Gierke disease IA ... enlarged liver
# Von Gierke disease IB ... enlarged liver
TopW
# WAGR Syndrome ... Splenomegaly
# Waldenström Macroglobulinemia ... enlarged spleen, enlarged liver
# Waldenstrom macroglobulinemia ... Splenomegaly
# Wandering spleen ... Splenomegaly, enlarged spleen
# Warm-reacting-antibody haemolytic anemia ... Splenomegaly
# Warm-reacting-antibody hemolytic anemia ... enlarged spleen
# Weber-Christian disease ... enlarged spleen
# Weil syndrome ... enlarged liver
# Weil's syndrome ... Splenomegaly
# Weinstein Kliman Scully syndrome ... Splenomegaly
# Wilson's Disease ... swollen liver, enlarged spleen, enlarged liver, swollen spleen
# Wolcott-Rallison syndrome ... enlarged spleen, enlarged liver
# Wolman disease ... Splenomegaly
# Wolman syndrome ... enlarged spleen, enlarged liver
# WT limb blood syndrome ... Splenomegaly
# Wyatt disease ... enlarged liver
TopX
# X-linked alpha thalassemia mental retardation syndrome (ATR-X) ... Splenomegaly
# X-linked lymphoproliferative syndrome ... Splenomegaly, enlarged spleen, enlarged liver
# X-linked sideroblastic anemia ... Splenomegaly, enlarged spleen, enlarged liver
# Xerocytosis, heriditary ... Hepatosplenomegaly
TopZ
# ZAP70 deficiency ... Splenomegaly
# Zellweger Syndrome ... enlarged liver
# Zellweger-like syndrome, without peroxisomal anomalies ... enlarged liver
# Zimmerman-Laband syndrome ... Splenomegaly, enlarged spleen, enlarged liver
TopConditions listing medical complications: Enlarged liver and spleen:
The following list of medical conditions have 'Enlarged liver and spleen' or similar listed as a medical complication in our database. This computer-generated list of complications may be inaccurate or incomplete. Always seek prompt professional medical advice about the cause of any symptom.
TopB
# Biliary atresia, intrahepatic, non syndromic form ... enlarged spleen
# Biliary atresia, intrahepatic, syndromic form ... enlarged spleen
TopH
# Hemochromatosis ... enlarged liver
# Hereditary hemorrhagic telangiectasia ... enlarged liver
TopI
# Infantile sialic acid storage disorder ... enlarged spleen, enlarged liver
# Infectious myocarditis ... enlarged liver
TopM
# Malaria ... enlarged spleen, enlarged liver
TopP
# Portal hypertension ... enlarged spleen
TopS
# Sickle Cell Anemia ... spleen enlargement
==External links==
* {{GPnotebook|1516961800}}
* {{Medcyclopaedia|vii/h/HEPATOSPLENOMEGALY}}
[[Category:Medical signs]]
[[Category:Hepatology]]
{{med-sign-stub}}
{{Digestive system and abdomen symptoms and signs}}
[[cs:Hepatosplenomegalie]]
[[de:Hepatosplenomegalie]]
[[fr:Hépatosplénomégalie]]
[[pl:Hepatosplenomegalia]]
[[pt:Hepatoesplenomegalia]]