Taussig-Bing syndrome
3417998
146171024
2007-07-21T18:57:45Z
Arcadian
104523
infobox
{{Infobox_Disease |
Name = {{PAGENAME}} |
Image = |
Caption = |
DiseasesDB = 32215 |
ICD10 = {{ICD10|Q|20|1|q|20}} |
ICD9 = {{ICD9|745.11}} |
ICDO = |
OMIM = 217095 |
MedlinePlus = |
eMedicineSubj = ped |
eMedicineTopic = 2509 |
eMedicine_mult = {{eMedicine2|ped|2508}} |
MeshID = D004310 |
}}
'''Taussig-Bing syndrome''' is a [[cyanotic heart defect|cyanotic]] [[congenital]] [[congenital heart defect|heart defect]] ('''CHD''') in which the patient has both [[double outlet right ventricle]] ('''DORV''') and [[subpulmonic]] [[ventricular septal defect]] ('''VSD''').
In DORV, instead of the normal situation where blood from the [[left ventricle]] ('''LV''') flows out to the [[aorta]] and blood from the [[right ventricle]] ('''RV''') flows out to the [[pulmonary artery]], both [[aorta]] and [[pulmonary artery]] are connected to the RV, and the only path for blood from the LV is across the VSD. When the VSD is [[subpulmonic]] (sitting just below the pulmonary artery), the LV blood then flows preferentially to the pulmonary artery. Then the RV blood, by default, flows mainly to the aorta.
The clinical manifestations of a Taussig-Bing anomaly, therefore, are much like those of [[dextro-Transposition of the great arteries]] (but the surgical repair is different).
[[Category:Congenital heart disease]]
{{circulatory-stub}}
{{Congenital malformations and deformations of circulatory system}}